{"id":142806,"date":"2023-04-12T07:58:11","date_gmt":"2023-04-12T07:58:11","guid":{"rendered":"https:\/\/labinsights.com\/acf_article\/%e8%a1%80%e5%8f%8b%e7%97%85%e8%a8%ba%e6%96%ad%e3%81%a8%e6%b2%bb%e7%99%82%e3%81%a7%e3%80%81%e3%80%8c%e3%81%99%e3%81%b9%e3%81%a6%e3%81%ae%e4%ba%ba%e3%81%b8%e3%81%ae%e3%82%a2%e3%82%af%e3%82%bb%e3%82%b9\/"},"modified":"2026-01-09T05:14:36","modified_gmt":"2026-01-09T05:14:36","slug":"how-haemophilia-diagnostics-and-treatments-help-drive-access-for-all","status":"publish","type":"acf_article","link":"https:\/\/labinsights.com\/ja\/disease-area\/coagulation\/how-haemophilia-diagnostics-and-treatments-help-drive-access-for-all\/","title":{"rendered":"\u8840\u53cb\u75c5\u8a3a\u65ad\u3068\u6cbb\u7642\u3067\u3001\u300c\u3059\u3079\u3066\u306e\u4eba\u3078\u306e\u30a2\u30af\u30bb\u30b9\u300d\u3092\u4fc3\u9032\u3059\u308b\u65b9\u6cd5"},"content":{"rendered":"<p>4\u670817\u65e5\u306f<a href=\"https:\/\/wfh.org\/world-hemophilia-day\/\" target=\"_blank\" 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class=\"text-align-justify\" style=\"font-family: Inter !important; font-weight: 500 !important; font-size: 28px !important; line-height: 36px !important; letter-spacing: 0px !important;\">\u75c5\u6c17\u306e\u8a3a\u65ad\u3068\u30ad\u30e3\u30ea\u30a2\u72b6\u614b\u306e\u8a55\u4fa1<\/h2>\n<p> 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Women&#8217;s and Children&#8217;s Hospital\u306e\u8840\u6db2\u5b66\/\u816b\u760d\u5b66\u30b5\u30fc\u30d3\u30b9\u306e\u30b7\u30cb\u30a2\u30b3\u30f3\u30b5\u30eb\u30bf\u30f3\u30c8\u3067\u3001\u540c\u9662\u306e\u8840\u6db2\u5b66\u691c\u67fb\u5ba4\u304a\u3088\u3073\u8840\u6db2\u30d0\u30f3\u30af\u3082\u30ea\u30fc\u30c9\u3059\u308bAssociate Professor Joyce Lam\u306f\u8ff0\u3079\u3066\u3044\u307e\u3059\u3002\u300c\u5148\u5929\u6027\u51fa\u8840\u969c\u5bb3\u306f\u3001\u51fa\u8840\u75c7\u72b6\u3092\u5448\u3059\u308b\u60a3\u8005\u306e\u6700\u3082\u4e00\u822c\u7684\u306a\u9451\u5225\u8a3a\u65ad\u306e\u4e2d\u306b\u306f\u542b\u307e\u308c\u3066\u3044\u306a\u3044\u53ef\u80fd\u6027\u304c\u3042\u308a\u3001\u3053\u308c\u306f\u3001\u3053\u308c\u3089\u304c\u7a00\u306a\u75c7\u72b6\u3068\u8003\u3048\u3089\u308c\u308b\u305f\u3081\u3067\u3059\u3002\u3053\u308c\u3089\u306e\u5148\u5929\u6027\u51fa\u8840\u72b6\u614b\u3092\u76e3\u8996\u3059\u308b\u305f\u3081\u306e\u533b\u7642\u63d0\u4f9b\u8005\u306e\u6559\u80b2\u306f\u975e\u5e38\u306b\u91cd\u8981\u3067\u3059\u3002\u300d\u3068\u540c\u6c0f\u306f\u4ed8\u3051\u52a0\u3048\u307e\u3059\u3002\u00a0\u00a0\u300c\u4e00\u65e6\u3001\u540c\u4e00\u5bb6\u7cfb\u5185\u306e\u7537\u6027\u60a3\u8005\u3068\u5973\u6027\u4fdd\u56e0\u8005\u306e\u53ef\u80fd\u6027\u304c\u3042\u308b\u8005\u3092\u540c\u5b9a\u3059\u308b\u305f\u3081\u306b\u3001\u5bb6\u7cfb\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u3092\u52e7\u3081\u308b\u3079\u304d\u3067\u3059\u3002\u300d\u8840\u53cb\u75c5\u306a\u3069\u306e\u5148\u5929\u6027\u51fa\u8840\u6027\u75be\u60a3\u3092\u8a3a\u65ad\u3059\u308b\u305f\u3081\u306b\u7528\u3044\u3089\u308c\u308b\u691c\u67fb\u306f\u3001\u304b\u306a\u308a\u4e00\u822c\u7684\u306a\u3082\u306e\u3067\u3042\u308a\u3001\u4e16\u754c\u4e2d\u306e\u81e8\u5e8a\u691c\u67fb\u5ba4\u3067\u4e00\u8cab\u3057\u3066\u4f7f\u7528\u3055\u308c\u3066\u3044\u307e\u3059\u3002\u6a19\u6e96\u7684\u306a\u8840\u7b97\u304b\u3089\u3001PT\u3001APTT\u3001\u304a\u3088\u3073\u30d5\u30a3\u30d6\u30ea\u30ce\u30fc\u30b2\u30f3\u306a\u3069\u306e\u4e00\u9023\u306e\u51dd\u56fa\u8a3a\u65ad\u307e\u3067\u3001\u8840\u53cb\u75c5\u306a\u3069\u306e\u51fa\u8840\u6027\u75be\u60a3\u306e\u65e5\u5e38\u7684\u306a\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u3067\u4f7f\u7528\u3055\u308c\u308b\u591a\u304f\u306e\u8a66\u9a13\u304c\u3042\u308a\u307e\u3059\uff08\u8a3a\u65ad\u30d5\u30ed\u30fc\u306e\u8a73\u7d30\u306a\u6982\u8981\u306b\u3064\u3044\u3066\u306f\u3001<a href=\"https:\/\/labinsights.com\/ja\/disease-area\/rare-diseases\/haemophilia-diagnostics-and-therapeutics-a-brief-introduction\/\" target=\"_blank\" rel=\"noopener\">Haemophilia diagnostics and treatments: a brief introduction 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Professor Lam\u306f\u8a00\u3044\u307e\u3059\u3002\u3053\u3046\u3057\u305f\u80af\u5b9a\u7684\u306a\u7d50\u679c\u306f\u3001\u9577\u5e74\u306b\u308f\u305f\u308b\u8840\u53cb\u75c5\u51e6\u7f6e\u306e\u9032\u5316\u306b\u3088\u3063\u3066\u652f\u6301\u3055\u308c\u3066\u304d\u307e\u3057\u305f\u3002\u907a\u4f1d\u5b50\u7642\u6cd5\u3092\u542b\u3080\u65b0\u3057\u3044\u6cbb\u7642\u6cd5\u304c\u8fd1\u5e74\u767a\u8868\u3055\u308c\u3066\u3044\u307e\u3059\u304c\u3001\u73fe\u5728\u3059\u3079\u3066\u306e\u56fd\u3067\u5229\u7528\u3067\u304d\u308b\u308f\u3051\u3067\u306f\u306a\u304f\u3001<a href=\"https:\/\/labinsights.com\/ja\/disease-area\/rare-diseases\/emerging-haemophilia-therapies-highlight-a-need-for-quality-diagnostics\/\" target=\"_blank\" rel=\"noopener\">\u65b0\u305f\u306a\u8840\u53cb\u75c5\u6cbb\u7642\u306f\u3001\u65b0\u3057\u3044\u6cbb\u7642\u6cd5\u306e\u6df1\u3044\u8b70\u8ad6\u306e\u305f\u3081\u306e\u8cea\u306e\u9ad8\u3044\u8a3a\u65ad<\/a>\u306e\u5fc5\u8981\u6027\u3092\u5f37\u8abf\u3057\u3066\u3044\u307e\u3059\u3002\u305d\u308c\u3067\u3082\u3001\u60a3\u8005\u306b\u3088\u308a\u826f\u597d\u306a\u8ee2\u5e30\u3092\u4e0e\u3048\u308b\u3067\u3042\u308d\u3046\u826f\u597d\u306a\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u3092\u7d99\u7d9a\u3059\u308b\u5fc5\u8981\u304c\u3042\u308a\u3001\u7406\u60f3\u7684\u306b\u306f\u518d\u767a\u6027\u306e\u88dc\u5145\u7642\u6cd5\u306e\u5fc5\u8981\u6027\u3092\u6392\u9664\u3057\u3066\u3044\u307e\u3059\u3002Associate Professor Lam\u306f\u30c1\u30fc\u30e0\u3068\u5171\u306b\u3001\u3088\u308a\u591a\u304f\u306e\u30c7\u30fc\u30bf\u3092\u53ce\u96c6\u3059\u308b\u3053\u3068\u3067\u3001\u8840\u53cb\u75c5\u60a3\u8005\u306e\u30b1\u30a2\u306e\u8cea\u3092\u5411\u4e0a\u3055\u305b\u308b\u3053\u3068\u3092\u76ee\u6307\u3057\u3066\u3044\u307e\u3059\u3002\u300c\u79c1\u305f\u3061\u306f\u3001\u6cbb\u7642\u6226\u7565\u306e\u8cea\u3092\u3088\u308a\u826f\u304f\u8a55\u4fa1\u3057\u3001\u60a3\u8005\u306e\u30b1\u30a2\u306e\u57fa\u6e96\u3092\u7d99\u7d9a\u7684\u306b\u6539\u5584\u3067\u304d\u308b\u3088\u3046\u306b\u3001\u5168\u56fd\u898f\u6a21\u3067\u51fa\u8840\u6027\u969c\u5bb3\u306e\u79c1\u305f\u3061\u306e\u30b3\u30db\u30fc\u30c8\u306e\u60a3\u8005\u767b\u9332\u3092\u4ecb\u3057\u3066\u533b\u7642\u60c5\u5831\u3068\u8ee2\u5e30\u30c7\u30fc\u30bf\u3092\u524d\u5411\u304d\u306b\u53ce\u96c6\u3059\u308b\u5fc5\u8981\u6027\u306b\u53d6\u308a\u7d44\u3093\u3067\u3044\u307e\u3059\u300d\u3068\u540c\u6c0f\u306f\u8a00\u3044\u307e\u3059\u3002\u8840\u53cb\u75c5\u60a3\u8005\u306f\u3001\u6ce8\u610f\u6df1\u3044\u30e2\u30cb\u30bf\u30ea\u30f3\u30b0\u3068\u9069\u5207\u306a\u6cbb\u7642\u306b\u3088\u308a\u3001\u6bd4\u8f03\u7684\u6b63\u5e38\u3067\u5145\u5b9f\u3057\u305f\u751f\u6d3b\u3092\u9001\u308b\u3053\u3068\u304c\u3067\u304d\u307e\u3059\u3002\u8a3a\u65ad\u691c\u67fb\u3068\u52b9\u679c\u7684\u306a\u6cbb\u7642\u3092\u901a\u3058\u3066\u60a3\u8005\u3092\u652f\u63f4\u3059\u308b\u3053\u3068\u306f\u3001\u81e8\u5e8a\u691c\u67fb\u5c02\u9580\u5bb6\u3068\u533b\u7642\u63d0\u4f9b\u8005\u306b\u3068\u3063\u3066\u9054\u6210\u53ef\u80fd\u306a\u76ee\u6a19\u3067\u3059\u3002<\/p>\n","protected":false},"excerpt":{"rendered":"<p>4\u670817\u65e5\u306f\u3001\u3053\u306e\u5e0c\u5c11\u75be\u60a3\u306b\u5bfe\u51e6\u3057\u3066\u3044\u308b\u4eba\u3005\u3068\u5bb6\u65cf\u3092\u79f0\u3048\u3001\u3053\u306e\u75be\u60a3\u306e\u610f\u8b58\u3092\u9ad8\u3081\u308b\u305f\u3081\u306b\u8a2d\u8a08\u3055\u308c\u305f\u56fd\u969b\u30ad\u30e3\u30f3\u30da\u30fc\u30f3\u3067\u3042\u308b\u4e16\u754c\u8840\u53cb\u75c5\u306e\u65e5\u3067\u3059\u3002\u4eca\u5e74\u306e\u30ad\u30e3\u30f3\u30da\u30fc\u30f3\u3067\u306f\u3001\u300c\u3059\u3079\u3066\u306e\u4eba\u3078\u306e\u30a2\u30af\u30bb\u30b9\uff1a\u51fa\u8840\u306e\u4e88\u9632\u3092\u4e16\u754c\u6a19\u6e96\u306e\u6cbb\u7642\u3068\u3057\u3066\u300d\u3068\u3001\u6cbb\u7642\u304c\u30b0\u30ed\u30fc\u30d0\u30eb\u306b\u5229\u7528\u53ef\u80fd\u3067\u3042\u308b\u3053\u3068\u3092\u78ba\u8a8d\u3059\u308b\u3053\u3068\u306b\u7126\u70b9\u3092\u5f53\u3066\u3066\u3044\u307e\u3059\u3002\u81e8\u5e8a\u691c\u67fb\u8a3a\u65ad\u306f\u3001\u3053\u306e\u76ee\u6a19\u3092\u9054\u6210\u3059\u308b\u4e0a\u3067\u91cd\u8981\u306a\u5f79\u5272\u3092\u679c\u305f\u3059\u3053\u3068\u304c\u3067\u304d\u307e\u3059\u3002\u8840\u53cb\u75c5\u306f\u3001\u8840\u6db2\u4e2d\u306e\u51dd\u56fa\u56e0\u5b50\u304c\u4e0d\u5341\u5206\u306a\u305f\u3081\u306b\u51fa\u8840\u304c\u5236\u5fa1\u4e0d\u80fd\u3068\u306a\u308b\u3082\u306e\u3067\u3059\u3002\u5178\u578b\u7684\u306b\u306f\u7b2cVIII\u56e0\u5b50\uff08\u8840\u53cb\u75c5A\uff09\u307e\u305f\u306f\u7b2cIX\u56e0\u5b50\uff08\u8840\u53cb\u75c5B\uff09\u306e\u6fc3\u5ea6\u304c\u4f4e\u304f\u3001\u6fc3\u5ea6\u304c\u4f4e\u4e0b\u3059\u308b\u306b\u3064\u308c\u3066\u75be\u60a3\u306e\u91cd\u75c7\u5ea6\u304c\u5897\u3057\u307e\u3059\u3002\u8840\u53cb\u75c5\u306e\u4eba\u306f\u3001\u305f\u3068\u3048\u5c0f\u3055\u306a\u50b7\u3067\u3082\u5371\u967a\u3068\u306a\u308a\u3001\u624b\u8853\u304c\u975e\u5e38\u306b\u56f0\u96e3\u306a\u3053\u3068\u3082\u3042\u308a\u307e\u3059\u3002\u95a2\u7bc0\u5185\u3067\u81ea\u7136\u51fa\u8840\u304c\u8d77\u3053\u308b\u3053\u3068\u3082\u3042\u308a\u3001\u6162\u6027\u95a2\u7bc0\u75db\u3092\u6765\u3057\u307e\u3059\u3002\u4e16\u754c\u4e2d\u306720\u4e07\u4eba\u4ee5\u4e0a\u306e\u4eba\u3005\u304c\u8840\u53cb\u75c5\u3068\u5171\u306b\u751f\u6d3b\u3057\u3066\u3044\u307e\u3059\u3002\u305d\u308c\u306f\u307e\u308c\u306a\u51fa\u8840\u6027\u969c\u5bb3\u3067\u3059\u304c\u3001\u4e16\u754c\u306e\u8840\u53cb\u75c5\u30b3\u30df\u30e5\u30cb\u30c6\u30a3\u304b\u3089\u306e\u30a2\u30c9\u30dc\u30ab\u30b7\u30fc\u306f\u3001\u3053\u306e\u75c7\u72b6\u306b\u3064\u3044\u3066\u5e83\u7bc4\u306a\u8a8d\u77e5\u6d3b\u52d5\u3092\u59cb\u3081\u307e\u3057\u305f\u3002\u8840\u53cb\u75c5\u306f\u3001X\u9023\u9396\u52a3\u6027\u5909\u7570\u4f53\u306b\u95a2\u9023\u3059\u308b\u305f\u3081\u3001\u5973\u6027\u3088\u308a\u3082\u7537\u6027\u306b\u304a\u3044\u3066\u4e00\u822c\u7684\u3067\u3059\u3002\u8840\u53cb\u75c5\u306e\u4eba\u306e\u307b\u3068\u3093\u3069\u306f\u3001\u751f\u307e\u308c\u3064\u304d\u8840\u53cb\u75c5\u3067\u3059\u304c\u3001\u81ea\u7136\u306b\u767a\u75c7\u3059\u308b\u3053\u3068\u3082\u3042\u308a\u307e\u3059\u3002\u6700\u8fd1\u767a\u8868\u3055\u308c\u305f\u8840\u53cb\u75c5\u306b\u5bfe\u3059\u308b\u65b0\u898f\u6cbb\u7642\u6cd5\u306b\u3088\u308a\u3001\u533b\u7642\u5f93\u4e8b\u8005\u30b3\u30df\u30e5\u30cb\u30c6\u30a3\u5185\u3067\u306f\u3001\u3053\u306e\u6cbb\u7642\u6cd5\u3078\u306e\u60a3\u8005\u30a2\u30af\u30bb\u30b9\u3092\u6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Women&#8217;s and Children&#8217;s Hospital\u306e\u8840\u6db2\u5b66\/\u816b\u760d\u5b66\u30b5\u30fc\u30d3\u30b9\u306e\u30b7\u30cb\u30a2\u30b3\u30f3\u30b5\u30eb\u30bf\u30f3\u30c8\u3067\u3001\u540c\u9662\u306e\u8840\u6db2\u5b66\u691c\u67fb\u5ba4\u304a\u3088\u3073\u8840\u6db2\u30d0\u30f3\u30af\u3082\u30ea\u30fc\u30c9\u3059\u308bAssociate Professor Joyce Lam\u306f\u8ff0\u3079\u3066\u3044\u307e\u3059\u3002\u300c\u5148\u5929\u6027\u51fa\u8840\u969c\u5bb3\u306f\u3001\u51fa\u8840\u75c7\u72b6\u3092\u5448\u3059\u308b\u60a3\u8005\u306e\u6700\u3082\u4e00\u822c\u7684\u306a\u9451\u5225\u8a3a\u65ad\u306e\u4e2d\u306b\u306f\u542b\u307e\u308c\u3066\u3044\u306a\u3044\u53ef\u80fd\u6027\u304c\u3042\u308a\u3001\u3053\u308c\u306f\u3001\u3053\u308c\u3089\u304c\u7a00\u306a\u75c7\u72b6\u3068\u8003\u3048\u3089\u308c\u308b\u305f\u3081\u3067\u3059\u3002\u3053\u308c\u3089\u306e\u5148\u5929\u6027\u51fa\u8840\u72b6\u614b\u3092\u76e3\u8996\u3059\u308b\u305f\u3081\u306e\u533b\u7642\u63d0\u4f9b\u8005\u306e\u6559\u80b2\u306f\u975e\u5e38\u306b\u91cd\u8981\u3067\u3059\u3002\u300d\u3068\u540c\u6c0f\u306f\u4ed8\u3051\u52a0\u3048\u307e\u3059\u3002\u00a0\u00a0\u300c\u4e00\u65e6\u3001\u540c\u4e00\u5bb6\u7cfb\u5185\u306e\u7537\u6027\u60a3\u8005\u3068\u5973\u6027\u4fdd\u56e0\u8005\u306e\u53ef\u80fd\u6027\u304c\u3042\u308b\u8005\u3092\u540c\u5b9a\u3059\u308b\u305f\u3081\u306b\u3001\u5bb6\u7cfb\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u3092\u52e7\u3081\u308b\u3079\u304d\u3067\u3059\u3002\u300d\u8840\u53cb\u75c5\u306a\u3069\u306e\u5148\u5929\u6027\u51fa\u8840\u6027\u75be\u60a3\u3092\u8a3a\u65ad\u3059\u308b\u305f\u3081\u306b\u7528\u3044\u3089\u308c\u308b\u691c\u67fb\u306f\u3001\u304b\u306a\u308a\u4e00\u822c\u7684\u306a\u3082\u306e\u3067\u3042\u308a\u3001\u4e16\u754c\u4e2d\u306e\u81e8\u5e8a\u691c\u67fb\u5ba4\u3067\u4e00\u8cab\u3057\u3066\u4f7f\u7528\u3055\u308c\u3066\u3044\u307e\u3059\u3002\u6a19\u6e96\u7684\u306a\u8840\u7b97\u304b\u3089\u3001PT\u3001APTT\u3001\u304a\u3088\u3073\u30d5\u30a3\u30d6\u30ea\u30ce\u30fc\u30b2\u30f3\u306a\u3069\u306e\u4e00\u9023\u306e\u51dd\u56fa\u8a3a\u65ad\u307e\u3067\u3001\u8840\u53cb\u75c5\u306a\u3069\u306e\u51fa\u8840\u6027\u75be\u60a3\u306e\u65e5\u5e38\u7684\u306a\u30b9\u30af\u30ea\u30fc\u30cb\u30f3\u30b0\u3067\u4f7f\u7528\u3055\u308c\u308b\u591a\u304f\u306e\u8a66\u9a13\u304c\u3042\u308a\u307e\u3059\uff08\u8a3a\u65ad\u30d5\u30ed\u30fc\u306e\u8a73\u7d30\u306a\u6982\u8981\u306b\u3064\u3044\u3066\u306f\u3001Haemophilia diagnostics and treatments: a brief introduction 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Professor Lam\u306f\u8a00\u3044\u307e\u3059\u3002\u3053\u3046\u3057\u305f\u80af\u5b9a\u7684\u306a\u7d50\u679c\u306f\u3001\u9577\u5e74\u306b\u308f\u305f\u308b\u8840\u53cb\u75c5\u51e6\u7f6e\u306e\u9032\u5316\u306b\u3088\u3063\u3066\u652f\u6301\u3055\u308c\u3066\u304d\u307e\u3057\u305f\u3002\u907a\u4f1d\u5b50\u7642\u6cd5\u3092\u542b\u3080\u65b0\u3057\u3044\u6cbb\u7642\u6cd5\u304c\u8fd1\u5e74\u767a\u8868\u3055\u308c\u3066\u3044\u307e\u3059\u304c\u3001\u73fe\u5728\u3059\u3079\u3066\u306e\u56fd\u3067\u5229\u7528\u3067\u304d\u308b\u308f\u3051\u3067\u306f\u306a\u304f\u3001\u65b0\u305f\u306a\u8840\u53cb\u75c5\u6cbb\u7642\u306f\u3001\u65b0\u3057\u3044\u6cbb\u7642\u6cd5\u306e\u6df1\u3044\u8b70\u8ad6\u306e\u305f\u3081\u306e\u8cea\u306e\u9ad8\u3044\u8a3a\u65ad\u306e\u5fc5\u8981\u6027\u3092\u5f37\u8abf\u3057\u3066\u3044\u307e\u3059\u3002\u305d\u308c\u3067\u3082\u3001\u60a3\u8005\u306b\u3088\u308a\u826f\u597d\u306a\u8ee2\u5e30\u3092\u4e0e\u3048\u308b\u3067\u3042\u308d\u3046\u826f\u597d\u306a\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u3092\u7d99\u7d9a\u3059\u308b\u5fc5\u8981\u304c\u3042\u308a\u3001\u7406\u60f3\u7684\u306b\u306f\u518d\u767a\u6027\u306e\u88dc\u5145\u7642\u6cd5\u306e\u5fc5\u8981\u6027\u3092\u6392\u9664\u3057\u3066\u3044\u307e\u3059\u3002Associate Professor 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